Zamoyo zathanzi zimatetezedwa ndi maselo a chitetezo cha m'thupi kuchokera ku mavairasi, fungal ndi mabakiteriya, zizindikiro ndi zina zosautsa. Matenda akuluakulu oyambitsa matenda osokoneza thupi amalepheretsa munthu kukhala ndi vutoli kuyambira zaka zoyambirira za moyo wake, koma akhoza kudziwonetsera yekha. Matendawa amafunika kuyang'anitsitsa nthawi zonse ndi katswiri komanso chithandizo cha nthawi yayitali.
Chiwerengero cha zikuluzikulu zapachiyambi
Matenda omwe akuganiziridwa ndi mitundu 5, yomwe imayambitsidwa chifukwa cha kusowa kwake:
1. Kusakhudzidwa kwa chitetezo cha ma selo:
- oroticide;
- matenda a Di Georgi;
- fermentopathy wodalira biotin;
- kusakwanira kwa purinucleoside phosphorylase.
2. Phagocytic primary immunodeficiency:
- matenda aakulu;
- cyclic ndi matenda acyclic neutropenia;
- Matenda a Miller ("leukocyte waulesi".
3. Kusakwanira kwa maselo osangalatsa:
- kuchepetsa chitetezo chamthupi;
- Matenda a Bruton;
- kusankha zosowa za immunoglobulins.
4. Kufooka kwakukulu kwa makompyuta ndi makoswe:
- Matenda a Wiskott-Aldrich;
- chithandizo ;
- chithandizo;
- Matenda a Glanzmann-Riniker.
5. kulephera kwowonjezera:
- Edema wa Quincke-Osler;
- lupus erythematosus;
- nyamakazi ya nyamakazi.
Zizindikiro za chimbudzi chachikulu
Palibe zizindikiro zomwe zimapangitsa kufotokoza molondola zomwe zimafotokozedwa ndi ma genetic. Mawonetseredwe a chipatala amasiyana kwambiri malingana ndi mtundu, mawonekedwe ndi kuopsa kwa matendawa.
Kukayikira kuti njira yoyamba yotetezera thupi m'thupi imatha kukhala zizindikiro zotere:
- kudwala matenda opatsirana komanso mavairasi;
- zotsatira zochepa zothandizira maantibayotiki;
- candidiasis wa khungu ndi kubwereranso;
- ziphuphu zoopsa;
- chibayo 2 ndi nthawi zambiri pachaka;
- okhazikika otitis, sinusitis, bronchitis.
Chithandizo cha primary immunodeficiency
Mankhwalawa ndi ovuta, chifukwa simungathe kuchiza matenda. Pofuna kusintha umoyo wa odwala, chithandizo chamankhwala nthawi zonse ndi immunoglobulins n'chofunikira, komanso kusankha mosamala antibacterial, antiviral ndi antimycotic wothandizira matenda.
Thandizo lachidziwitso la matendawa limaphatikizapo kupatsirana mafupa a mitsempha, zomwe zimachitidwa bwino ali wamng'ono. Koma ndikuyenera kuzindikira kuti opaleshoniyi ndi yokwera mtengo kwambiri, ndipo nthawi zina zimakhala zovuta kupeza woperekayo mokwanira.