Cystic fibrosis

Chovuta kwambiri kuchiza ndi matenda obadwa nawo omwe amakhudzana ndi kusintha kwa majini. Matenda oterewa ndi a cystic fibrosis, omwe ali ndi kuchulukana kwakukulu komanso maphunziro osatha. Pali mitundu yosiyanasiyana ya matendawa, amagawidwa malinga ndi chigawo ndi momwe kugonjetsedwa kwa ziwalo za mkati.

Kodi cystic fibrosis kapena cystic fibrosis n'chiyani?

Matendawa akufotokozedwa ndi kusintha kwa jini la CFTR lomwe limayambitsa kuyamwa kwa mchere. Chifukwa cha kusintha kwake, kusungunuka kumabisika, komwe kumatulutsa mitundu yosiyanasiyana ya thupi m'thupi. Chifukwa chodya kwambiri mchere mumaselo, komanso kusowa kwa madzi, chimbudzi chimakhala chovuta ndipo chimakhala m'matope, kuziphimba. Patapita kanthawi pa tsamba la "traffic jams" zoterezi amapangidwa.

Pali mitundu itatu yaikulu ya cystic fibrosis:

Pali mbali zina zomwe zimakhudza matendawa, mwachitsanzo, pali cystic fibrosis ya lacteal ndi mapascita, macimo a paranasal. Iwo amapezeka kawirikawiri, koma osakhala oopsa kuposa mitundu ina yapamwamba ya matenda obadwa nawo.

Zizindikiro za cystic fibrosis

Zizindikiro za cystic fibrosis zimadalira chiwindi ndi mtundu wa matendawo, komanso kukula kwake.

Cystic fibrosis ya mapapo amasonyezedwa motere:

Maonekedwe a m'mimba a cystic fibrosis akuphatikiza ndi zizindikiro zotsatirazi:

NthaƔi zambiri, ndi mtundu uwu wa cystic fibrosis, chiwindi chimakhudzidwa. Izi zimachitika chifukwa cha kuphwanya ndi kupweteka kwa ubongo m'matumbo, chifukwa cha zomwe zimayambira m'madzi, zomwe zimachititsa kuti kuyamba kwa cirrhosis.

Mtundu woopsa kwambiri wa cystic fibrosis umasakanikirana. Zimaphatikizapo zizindikiro za bronchopulmonary ndi matenda osokoneza ubongo nthawi imodzi.

Kuchiza kwa cystic fibrosis kapena cystic fibrosis

N'zosatheka kuchotsa matenda omwe akufotokozedwa kwamuyaya, komabe, ndi chithandizo choyenera chenicheni, umoyo wa munthu yemwe ali ndi cystic fibrosis wakula bwino kwambiri.

Kuwonjezera pa mankhwala omwe adalangizidwa ndi dokotala, wodwala ayenera kukonzekera bwino zakudya, nthawi zonse azichita masewera olimbitsa thupi, masewera olimbitsa thupi.