Amyloidosis wa impso

Impso za Amyloidosis ndizochepa kwambiri, zomwe zimawonedwa ndi kuphwanya mapuloteni-carbohydrate metabolism ndi mapangidwe ndi kuika m'matini a impso a mankhwala enaake - amyloid. Amyloid ndi puloteni yopangidwa ndi puloteni-polysaccharide, yofanana ndi wowuma, yomwe si yachilendo kwa thupi ndipo imasokoneza ntchito ya impso.

Mitundu ya amyloidosis ya impso

Pali mitundu yambiri ya amyloidosis:

Zifukwa za amyloidosis a impso

Nthawi zina, zimayambitsa kukula kwa matenda sizidziwika (primary amyloidosis). Mwazidzidzidzi zomwe zimayambitsa amyloidosis, matendawa amatha kusiyanitsa:

Kutenga nthawi yaitali kwa matenda aakulu kungachititse kusintha kosasintha kwa mapuloteni m'thupi. Chotsatira cha izi ndi mapangidwe a antigen mapuloteni - zinthu zakunja, zomwe zimayambitsa ma antibodies.

Zizindikiro za impso amyloidosis

Mapulogalamu a Amyloidosis amapezeka mu magawo atatu, omwe ali ndi mawonetseredwe ake:

  1. Kumayambiriro koyambirira - pakadali pano palibe mawonetseredwe aakulu a matendawa, makamaka kuchepa kwa ntchito, kufooka kwakukulu. Mu mkodzo umapezeka pang'ono puloteni (proteinuria), m'magazi - mkulu wa cholesterol. Ntchito za impso sizikusintha panthawi imeneyi.
  2. Mafuta (nephrotic) siteji - amadziwika ndi kupititsa patsogolo kwa edema, sclerosis ndi amyloidosis ya msuzi wamphongo, kukula kwa matenda a nephrotic. Pali chofunika kwambiri cha proteinuria, hypercholesterolemia, hypoproteinemia, ndipo nthawizina - kupweteka kwa magazi. Impso zimafutukuka, zimakhala zofiira, zimakhala zofiira za pinki.
  3. Gawo lotentha limagwirizana ndi chitukuko cha matenda osalimba. Pali zowonjezereka za edema, uremia, kutopa kwa thupi lonse, amyloidosis nthawi zambiri zimakhala zovuta ndi kupweteka kwa mitsempha yambiri ndi anuria ndi matenda.

Kuzindikira matenda a impso amyloidosis

Poyambirira, matendawa ndi ovuta kuwunikira. Kukayikira kuti chitukuko cha amyloidosis chikhoza kukhala chifukwa cha mayeso a labotale - kusanthula magazi ndi mkodzo. Kuchita pulogalamu kungakhalenso chizindikiro.

Kachipangizo kameneka kamtima kamatha kusonyeza mphamvu zochepetsetsa komanso zizindikiro zabodza za matenda a mtima. Impso ultrasound ingagwiritsidwe ntchito kuyesa kukula kwake.

Pofuna kutsimikizira kuti matendawa amapezeka, impso ya impso imagwiritsidwanso ntchito (kuyesa organ morphology), yomwe imathandiza kuti pakhale mawonekedwe a amyloid.

Kuchiza kwa amyloidosis a impso

Kuchiza kwa amyloidosis kumagwira ntchito pokhapokha pa gawo loyamba la chitukukocho. Cholinga chake ndicho kuthetsa zinthu zomwe zimathandiza kupanga mapulogalamu a amyloid, komanso poyimitsa kupanga mankhwalawa.

Ndi mankhwala achiwiri amyloidosis, mankhwala amathandiza kuthetsa matenda omwe amayambitsa matendawa. Izi zimagwiritsidwa ntchito.

Chofunika kwambiri pa chithandizo cha amyloidosis chimapatsidwa chakudya chomwe chimaperekedwa malinga ndi siteji ya matenda ndi zizindikiro za mayesero. Monga lamulo, zimayenera kuchepetsa kumwa mchere, mapuloteni, kuchuluka kwa zakudya zambiri za vitamini C ndi salt ya potaziyamu.

Mankhwala osokoneza bongo a amyloidosis a impso akuphatikizapo kuika mankhwala osiyanasiyana - antihistamines, anti-inflammatory, diuretic, etc. Renal dialysis ikulimbikitsidwa.