Sjogren's Syndrome - zonse zomwe zimapanga chithandizo

Matenda a Sjogren ndi matenda omwe amachititsa kuti thupi liwonongeke. Kuchokera pamatendawa, exocrine glands - mankhwala osweka ndi osweka - amavutika kwambiri. Kawirikawiri, matendawa amatha kupitirirabe.

Sjogren's Syndrome - kodi matendawa ndi otani?

Pa zovuta za zizindikiro za matenda owuma kwa nthawi yoyamba chidwicho chinaperekedwa ndi Swedish ophthalmologist Shegren zaka zosakwana zaka zana zapitazo. Anapeza odwala ambiri omwe anabwera kwa iye ndi zodandaula pamaso pake, zizindikiro zina zofanana: kutupa kosakanikirana kwa ziwalo ndi xerostomia - kuuma kwa mucosa. Kuwunika ena madokotala ndi asayansi. Zinaoneka kuti vutoli ndilofala ndipo kulimbana nalo kumafuna chithandizo china.

Matenda a Sjogren - ndi chiyani? Matendawa amadzimadzimadziwa amatsutsana ndi zolephera za chitetezo cha mthupi. Zamoyo zimatengera maselo awo kunja kwa maselo akunja ndikuyamba kumayambitsa ma antibodies. Malinga ndi chiyambi ichi, kutukuka kumayambira, komwe kumachepetsa kuchepa kwa ntchito za glands zomwe zimakhala kunja kwachinsinsi - kawirikawiri zimakhala zonyansa komanso zowopsya.

Sjogren's Syndrome - Zimayambitsa

Pofuna kudziwa mosapita m'mbali chifukwa chake matenda opangidwa ndi autoimmune amakula, mankhwala sangathe. Choncho, kumene matenda ouma a Sjogren amachokera ndi chinsinsi. Zimadziwika kuti majini, maumununi, mahomoni ndi zina zakunja zimagwira nawo ntchito pa chitukuko cha matendawa. Kawirikawiri, mavairasi monga cytomegalovirus, Epstein-Barr, herpes, kapena matenda monga polymyositis, systemic scleroderma, lupus erythematosus, nyamakazi ya nyamakazi imakhala yolimbikitsa kwambiri kuti chitukukochi chikule.

Primary Sjogren's Syndrome

Pali mitundu iwiri ikuluikulu ya matenda. Koma iwo ali ofanana. Kuyanika nsonga zamkati m'magulu onsewa kumayamba chifukwa cha kupweteka kwa mankhwala a exocrine pamatumbo a m'mimba ndi tsamba lakupuma. Ngati matendawa akukhala ngati matenda odziimira okha ndipo palibe chomwe chimayambitsa maonekedwe ake, ndiye kuti matendawa ndi ovuta kwambiri.

Sjogren's Syndrome yachiwiri

Monga momwe chiwonetsero chimasonyezera, nthawi zina, matendawa amachitikira kutsogolo kwa zizindikiro zina. Malingana ndi ziwerengero, matenda ena owuma amapezeka 20 - 25% mwa odwala. Amayika pamene matendawa amakumana ndi vuto la matenda a rhumum, dermatomyositis, scleroderma ndi zina zogwirizana ndi zilonda zamtundu wogwirizana.

Matenda a Sjogren - zizindikiro

Mawonetseredwe onse a matendawa amagawanika kukhala amchere komanso owonjezera. Mfundo yakuti Sjogren's syndrome yafalikira kumatenda otupa amatha kumvetsetsa ndi "kuwombera" mchenga m'maso. Ambiri akudandaula za khungu lakuthwa kwambiri. Nthawi zambiri maso amawoneka ofiira, ndipo m'makona a iwo amasonkhanitsa mankhwala owoneka bwino. Pamene matendawa akuyamba, photophobia ikuyamba, diso limangoyang'ana mozama, maonekedwe akuwonongeka. Kuwonjezeka kwa malembo opweteka ndi chinthu chosavuta.

Makhalidwe omwe ali ndi matenda a Sjogren, omwe amakhudzidwa ndi matenda osakanikirana: madzi owopsa mumkamwa, malire ofiira, milomo. Kawirikawiri, odwala amayamba kugunda , ndipo, pambali pa zovuta zazing'ono, madontho ena oyandikana nawo amakhalanso akuwonjezeka. Poyamba, matendawa amangodziwoneka ndi kuumirira thupi kapena kupsinjika maganizo. Koma kenaka kuuma kumakhala kwamuyaya, milomo imakhala ndi mafinya omwe amachititsa kuti pakhale chiopsezo cholowa ndi matendawa.

Nthawi zina, chifukwa chouma mu nasopharynx, ziphuphu zimayamba kupanga mphuno ndi mitsempha, zomwe zingapangitse otitis komanso kuchepa kwachangu. Pamene zingwe zamagetsi ndi zowonjezereka zimagonjetsedwa kwambiri, zimakhala zowonjezereka. Ndipo zimakhalanso kuti kuphulika kwa kumeza kumatsogolera ku matendawa. Chidziwitsochi chikuwonetsedwa ndi kunyozetsa, kuwonjezereka kwa njala, kulemera kwa chigawo cha epigastric dera likatha kudya.

Mawonetseredwe apadera a mawonekedwe a chizindikiro cha Sjogren's syndrome akuwoneka ngati awa:

Matenda a Sjogren - matenda osiyanasiyana

Tsatanetsatane wa matendawa makamaka pamaziko a xerophthalmia kapena xerostomia. Zomalizazi zimapezeka mwa njira ya sialography, kujambula kwa parotid ndi chidziwitso chodzidzimutsa. Poyezetsa matenda a xerophthalmia, mayeso a Schirmer amachitika. Mapeto amodzi a pepala lopukuta amaikidwa pansi pa khungu lakuya ndikusiya kwa kanthawi. Mu anthu abwinobwino, patatha pafupifupi mphindi zisanu, pafupifupi 15 mm pamphepeteyo idzakhala yonyowa. Ngati matenda a Sjogren akutsimikiziridwa, matendawa amasonyeza kuti si oposa 5 mm wet.

Kuzindikiritsa kusiyana kwabwino ndikofunika kukumbukira kuti NLS ikhoza kukhala yofanana ndi matendawa monga autoimmune thyroiditis, percinosis magazi, matenda osokoneza bongo. Tsatanetsatane wa matenda oyambitsa wodwala amathandizidwa kwambiri ndi kupezeka kwa ma antibodies SS-B. Zimakhala zovuta kwambiri kupeza matenda a Sjogren ndi nyamakazi ya nyamakazi, chifukwa kuwonongeka kwa mgwirizano kumayambira nthawi yayitali kusanawoneke kwa zizindikiro zowuma.

Matenda a Sjogren - mayesero

Kuzindikira matendawa kumaphatikizapo kuyesa ma laboratory. Mukapeza kuti muli ndi matenda a Sjogren, zotsatirazi zimasonyeza pafupifupi zotsatira zotsatirazi:

  1. Mu kuyesa kwa magazi, kuthamanga kwa ESR, kuchepa kwa magazi ndi kuchepa kwa maselo oyera a magazi kumatsimikiziridwa.
  2. OAM imadziwika ndi kukhalapo kwa mapuloteni.
  3. Puloteni imayambanso kusanthula mwazi. Kuonjezerapo, phunziroli likuwulula maulendo ambiri a chifuwa chachikulu.
  4. Kuyesera kwapadera kwa magazi chifukwa cha kukhalapo kwa ma antibodies kwa thyroglobulin mu 35% kumasonyeza kuwonjezeka kwa ndondomeko yawo.
  5. Zotsatira za mankhwala amtundu wa salivary zimatsimikizira zizindikiro za matenda a Sjogren.

Sjögren's Syndrome - mankhwala

Ichi ndi vuto lalikulu, koma silikupha. Ngati mutamvetsera zizindikiro zake nthawi ndi pamene mukupeza kuti matenda a Sjogren ayamba, mungathe kukhala nawo, mumamva bwino. Chinthu chachikulu kwa odwala sichiyenera kuiwala za kufunikira kwa moyo wathanzi. Izi zidzakuthandizira kulimbikitsa chitetezo cha mthupi, sizidzalola kuti chizoloŵezi chokhala ndi vutoli chizikhala patsogolo komanso kuchepetsa kwambiri chiopsezo cha mavuto.

Kodi n'zotheka kuchiza matenda a Sjogren?

Chidziwitsocho chitatsimikiziridwa, wodwalayo amalandila malangizo othandizira. Matenda a Sjogren akuchiritsidwa bwino masiku ano, koma sizingatheke kuthetsa matendawa kwathunthu. Pachifukwachi, ndi mankhwala okhawo omwe amachiritsidwa. Zolinga zowunika chithandizo cha mankhwala ndizochizoloŵezi cha maonekedwe a matenda. Ngati zolinga zonse zothandizira, zisonyezo za labotolo ndi chithunzi chake chimapindulitsa.

Sjögren's Syndrome - Zipangizo Zamakono

Thandizo la matenda ouma limaphatikizapo kuchepetsa zizindikiro, ndipo ngati kuli kotheka, kulimbana ndi matenda omwe amadziwika nawo. Asanayambe kulandira matenda a Sjogren, matendawa amachitika. Pambuyo pake, monga lamulo, njira zoterezi zimagwiritsidwa ntchito:

Kuti muchotse pakamwa youma, yambani. Matenda a maso owuma amachizidwa ndi instillation ya saline, Hemodesis. Miphika yowuma yowonongeka imatha kuchiritsidwa ndi Bromhexine . Ndi kutupa kwa glands Dimexide, Hydrocortisone kapena Heparin akuvutika. Nthawi zina pakamwa youma pakadalidwa ndi matenda a Sjogren kumayambitsa matenda a mano. Pofuna kuwaletsa, muyenera kusamalira ukhondo wambiri.

Matenda a Sjogren - mankhwala ndi mankhwala ochiritsira

Matenda owuma ndi zovuta komanso zizindikiro. Ndi zonsezi ndi bwino kulimbana mwachikhalidwe. Koma nthawi zina ndi matenda a Sjogren, njira zamagulu zomwe zimagwiritsidwa ntchito mofanana zimathandiza kusintha mkhalidwe wa wodwalayo. Mwachitsanzo, odwala ena amadziŵa kuti madontho a diso opangidwa kuchokera ku katsabola ndi madzi a mbatata amakhala othandiza kwambiri kusiyana ndi mankhwala omwe amamwa mankhwala.

Kuchotsa mankhwala a zitsamba kwa rinsing

Zosakaniza:

Kukonzekera ndi ntchito:

  1. Grasss kusakaniza ndi mopepuka pogaya.
  2. Madzi wiritsani ndi kutsanulira mu youma osakaniza.
  3. Mankhwalawa amafunika kuswana kwa mphindi 40.
  4. Pambuyo kusinthasintha ndi okonzeka kugwiritsidwa ntchito.

Matenda a Sjogren - kulengeza

Matendawa amapitirira popanda kuopseza moyo. Koma chifukwa cha iye, umoyo wa odwala ukuwonongeka. Chithandizo chimathandiza kupewa mavuto komanso kumathandiza kuti akuluakulu azikhala ndi vuto labwino - Sjogren's syndrome kwa ana ndizovuta kwambiri. Ngati chithandizochi sichiyamba, matendawa akhoza kukhala ovuta kwambiri, omwe, ngati matenda achilendo, monga bronchopneumonia , sinusitis kapena tracheitis, nthawi zina amachititsa kulemala.