Neuroblastoma ya retroperitoneal space

Neuroblastoma ndi chotupa chachikulu chomwe chimakhudza dongosolo lachisomo lachisomo. Kawirikawiri, chotupacho chimapezeka kwa ana mpaka zaka ziwiri mu retroperitoneal space. Pankhaniyi, chitukuko cha matendawa chimayamba ndi adrenal glands. Komanso, chotupa chachikulu chingakhudze ziphuphu pamtunda wa msana - m'dera la thoracic ndi lachiberekero.

Zimayambitsa maonekedwe a neuroblastoma

Mpaka pano, asayansi sangathe kufotokoza momveka bwino chifukwa chake matenda owopsawa akuwonekera. Zimadziwika kuti neuroblastoma imayamba kuchokera ku maselo ammmoni, omwe amabadwa ndi mphutsi. Mizu ya matendawa imakhala mu ubongo ndi kusintha kwa maselo. Nthaŵi zina, kutupa m'mimba kumawoneka panthawi ya ultrasound.

Kodi zizindikiro za retroperitoneal neuroblastoma ndi ziti?

Chotupa choopsa chimakhala chowawa kwambiri ndipo chikhoza kukula mwamsanga, zomwe zimayambitsa mapangidwe a metastases. Ngakhale pali zovuta pamene mankhwala odzidzimutsa anayamba mwadzidzidzi popanda thandizo lachipatala. Komanso, mwa odwala ena, maselo owonongeka anasandulika kukhala maselo oopsa.

Neuroblastoma ya malo otchedwa retroperitoneal amachititsa kuwonjezeka kwa mimba ya mwanayo, nthawi zambiri kumapweteka ululu m'mimba mwa m'mimba.

Kawirikawiri, chotupacho chimayambitsa kudzikuza, kufooka kwa matumbo ndi chikhodzodzo. Kutentha kwa thupi ndi kuthamanga kwa magazi kungapitirire. Komanso, mwanayo akhoza kutaya njala, kulemera kwake mwamsanga.

Matenda a Neuroblastoma

Pofuna kuika matendawa ndi neuroblastoma ndikuyamba kulandira chithandizo choyenera, m'pofunika kuti muwone bwinobwino. Ndi neuroblastoma, kafukufuku wake wamagetsi amagwiritsidwa ntchito kwambiri, chotupa chonsecho ndi cha metastases.

Chofunika kumvetsetsa gawo la matendawa ndi ultrasound ndi computed tomography.

Magawo 4 a retroperitoneal neuroblastoma

Njira yowonjezeramo mankhwala ndi zotsatira zake mwachindunji zimadalira pa siteji ya matendawa. Zimavomerezedwa kusiyanitsa magawo anayi a matendawa. Koma muyenera kudziwa kuti ngati matendawa amatha kuchiritsidwa mu gawo loyamba kapena lachiwiri, ndiye kuti mwayi wafupika kwambiri mu gawo lachitatu ndi lachinayi. Tiyeni tione mwatsatanetsatane.

  1. ² gawo. N'zotheka kuchotsa mankhwala osokoneza bongo.
  2. YAM'MBUYO YOTSATIRA Mwina mwamsanga kuchotsedwa kwa neuroblastoma ambiri.
  3. IIB siteji. Neuroblastoma ikhoza kukhala imodzi. Pali kuthekera kwa kuchotsa kwathunthu, kapena zambiri za izo.
  4. Dzina loyamba. Panthawi imeneyi, chotupacho chingakhale chozungulira, chapakati, kapena kugunda mbali inayo. Komanso metastases mumatenda amadzimadzi amasonyezedwa. Sangathe kupulumutsa ana oposa 55-60%.
  5. IV. Kugonjetsedwa kwakukulu ndi metastases m'matumbo, mafupa ndi ziwalo zina. Amapulumuka osaposa kotala la ana odwala.
  6. IVS siteji. Amadziwika ndi zotupa m'zigawo zoyamba ndi ziwiri, komanso zimakhudza chiwindi, khungu ndi mafupa.

Neuroblastoma ndi matenda owopsa kwambiri. Njira zazikulu zothandizira - kuchotsedwa mwamsanga kwa maphunziro oopsa, chemotherapy ndi mankhwala omwe amatulutsa mankhwala.

Malingana ndi siteji ya matendawa, mankhwalawa amagwiritsidwa ntchito. Ngati matendawa ali pachigawo choyamba kapena chachiwiri, monga lamulo, opaleshoni yothandizidwa ndi mankhwala am'mbuyomu aperekedwa. Gawo lachitatu la chitukuko sichikhoza kugwira ntchito, choncho mwanayo amalembedwa mankhwala a chemotherapy. Pakati pachinayi, opaleshoni imagwiritsidwa ntchito ndikutsatiridwa ndi mafupa a mafupa. Ndikofunika kuti mudziwe matendawa pakapita nthawi. Poyambirira njirazo zimatengedwa, ndipamwamba mipata ya kuchira.